Russian veterinary journal Russian veterinary journal Российский ветеринарный журнал 2500-4379 51081 10.32416/2500-4379-2022-2-17-25 КЛИНИЧЕСКИЙ СЛУЧАЙ CASE REPORT КЛИНИЧЕСКИЙ СЛУЧАЙ Univentricular heart in a Maine Coon Единственный желудочек сердца у кота породы мейн-кун Кадырова Аделя Илмировна Kadyrova Adelya Ilmirovna kadyrovaai@yandex.ru Косенко Александр Ионович Kosenko Aleksandr Ionovich Илларионова Владислава Константиновна Illarionova Vladislava Konstantinovna

кандидат биологических наук;

candidate of sciences in biology;

 Ветеринарная клиника «Биоконтроль» Москва Россия Veterinary Clinic «Biocontrol» Moscow Russian Federation Национальный медицинский исследовательский центр сердечно-сосудистой хирургии им. Бакулева МЗ РФ Москва Россия A.N. Bakulev National Medical Research Center of Cardiovascular Surgery Moscow Russian Federation Ветеринарная клиника «Биоконтроль» Москва Россия Veterinary Clinic «Biocontrol» Moscow Russian Federation Федеральное государственное бюджетное образовательное учреждение высшего образования «Московская государственная академия ветеринарной медицины и биотехнологии — МВА имени К.И. Скрябина» Москва Россия Moscow State Academy of Veterinary Medicine and Biotechnology named after K.I. Skryabin Moscow Russian Federation Ветеринарная клиника «Корветцентр» Королев Россия Veterinary clinic "Corvetcenter" Korolev Russian Federation 11 07 2022 11 07 2022 2022 2 17 25 18 06 2022 https://logospress.editorum.ru/en/nauka/article/51081/view

Единственный желудочек сердца (ЕЖС) ― это редкая группа врожденных пороков сердца, характеризующаяся атриовентрикулярным соединением с одним желудочком. Двуприточный морфологический левый желудочек с вентрикуло-артериальной дискордантностью ― наиболее частая форма ЕЖС. Методы диагностики патологии включают в себя ЭхоКГ, АКГ и МРТ. У людей радикальным методом хирургического лечения является трансплантация сердца. Паллиативное хирургическое лечение представляет собой двух- или трехэтапную коррекцию порока с исключением рудиментарного желудочка из кровообращения. Медикаментозная терапия направлена на лечение СН и ЛГ. В статье описаны этапы диагностики и лечения ЕЖС у кота породы мейн-кун.

Univentricular heart (UH) is a rare group of congenital heart disease characterized by the atrial chambers connects with one ventricular chamber. The most frequent UH is double inlet morphologically left ventricle with the discordant ventriculo-arterial connection. The main diagnostic methods are echocardiography, angiocardiography and magnetic resonance imaging. In humans, heart transplantation is a radical method of surgical treatment. Palliative surgical management is different based on the underlying anatomy and include 2 or 3 stage defect correction with the exclusion of the rudimentary ventricle from the circulation. The focus of therapy is to management heart failure and pulmonary hypertension. The article describes the stages of diagnosis and treatment of UH in a Maine Coon.

 кошка единственный желудочек сердца легочная гипертензия мальпозиция магистральный сосудов врожденный порок сердца эхокардиография feline univentricular heart pulmonary hypertension malposition of the great arteries congenital heart disease echocardiography

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